What is Kasabach-Merritt syndrome

Kasabach-Merritt syndrome is a rare and potentially life-threatening condition characterized by the formation of abnormal blood vessels called hemangiomas. These hemangiomas can develop anywhere in the body, but are commonly found in the skin, liver, or other organs. The syndrome is typically diagnosed in infancy or early childhood.

The most significant feature of Kasabach-Merritt syndrome is the association of these hemangiomas with a severe decrease in platelet count, known as thrombocytopenia. This can lead to excessive bleeding and bruising. The syndrome may also cause anemia and clotting abnormalities.

The exact cause of Kasabach-Merritt syndrome is not fully understood, but it is believed to involve an abnormal growth of blood vessels. Treatment options for this condition are limited and often challenging. They may include medications to stabilize platelet levels, surgical removal of the hemangiomas, or other interventions to control bleeding.

Early diagnosis and prompt management are crucial in improving outcomes for individuals with Kasabach-Merritt syndrome. Close monitoring and collaboration between healthcare professionals are essential to provide appropriate care and support for affected individuals and their families.