Biliary Atresia, also known as "extrahepatic biliary atresia," is a rare and serious liver disease that primarily affects infants. It is characterized by the progressive destruction or absence of the bile ducts, which are responsible for carrying bile from the liver to the gallbladder and small intestine.
Biliary Atresia synonyms:
Biliary Atresia is a condition that typically becomes evident within the first few weeks to months of a baby's life. The exact cause of this disease is still unknown, but it is believed to involve a combination of genetic and environmental factors. Without prompt medical intervention, biliary atresia can lead to liver damage, cirrhosis, and ultimately, liver failure.
Early signs and symptoms of biliary atresia may include:
Diagnosis of biliary atresia involves various tests, such as blood tests, imaging studies, and a liver biopsy. The only definitive treatment for biliary atresia is a surgical procedure called the Kasai procedure or hepatoportoenterostomy. This procedure aims to restore bile flow by creating a connection between the liver and the small intestine.
If the Kasai procedure is successful, the infant may experience:
However, even with a successful Kasai procedure, many infants with biliary atresia will eventually require a liver transplant. Regular medical follow-up and ongoing care are crucial for managing the long-term effects of this condition.
In conclusion, biliary atresia, also referred to as extrahepatic biliary atresia, is a rare liver disease affecting infants. Early diagnosis and timely intervention are essential for improving outcomes and preventing severe liver damage.