Dejerine Sottas Disease, also known as Dejerine-Sottas neuropathy, is a rare genetic disorder that affects the peripheral nerves. It is named after the French neurologists Jules Dejerine and Pierre Marie Sottas, who first described the condition in the late 19th century.
This disease is characterized by the progressive degeneration of the peripheral nerves, which are responsible for transmitting signals between the brain and spinal cord to the rest of the body. As a result, individuals with Dejerine Sottas Disease experience muscle weakness, sensory loss, and impaired reflexes.
There are several synonyms used to refer to this condition:
It is important to note that while these terms are used interchangeably, they all refer to the same underlying condition - Dejerine Sottas Disease. The choice of terminology may vary depending on the medical professional or the specific context in which the disease is being discussed.