What is the prevalence of Ivemark Syndrome?
How many people does Ivemark Syndrome affect? Does it have the same prevalence in men and women? And in the different countries?
Ivemark Syndrome is a rare congenital disorder characterized by the absence or underdevelopment of certain organs on the left side of the body. It affects multiple systems, including the heart, spleen, and lungs. The prevalence of Ivemark Syndrome is extremely low, with only a few hundred cases reported worldwide. Due to its rarity, the exact prevalence is difficult to determine. However, it is considered to be a very rare condition. Ivemark Syndrome can have significant health implications and often requires specialized medical care.
Ivemark Syndrome, also known as asplenia with cardiovascular anomalies, is an extremely rare congenital disorder characterized by the absence or underdevelopment of the spleen, as well as various heart defects. The prevalence of Ivemark Syndrome is difficult to determine precisely due to its rarity and the lack of comprehensive data. However, it is estimated to occur in approximately 1 in 10,000 to 1 in 20,000 live births.
This syndrome is considered a complex condition with a wide range of associated abnormalities, including malformations of the heart, lungs, liver, and other organs. The absence of a spleen can lead to an increased risk of severe infections, particularly those caused by encapsulated bacteria.
Diagnosis of Ivemark Syndrome typically occurs during infancy or childhood, often due to the presence of heart defects or recurrent infections. Treatment involves managing the associated symptoms and complications, such as surgical interventions for heart abnormalities and preventive measures against infections.
Given the rarity of Ivemark Syndrome, it is crucial for affected individuals and their families to consult with medical professionals experienced in managing this condition to ensure appropriate care and support.
