Primary Intestinal Lymphangiectasia is a rare disorder characterized by abnormal dilation of the lymphatic vessels in the small intestine. These vessels are responsible for transporting lymph fluid, which contains fats and proteins, throughout the body. When these vessels become enlarged and dysfunctional, it leads to the leakage of lymph fluid into the intestinal lumen, resulting in malabsorption of fats and proteins.
Symptoms of Primary Intestinal Lymphangiectasia may include chronic diarrhea, abdominal pain, weight loss, and nutritional deficiencies. The condition is typically diagnosed through a combination of clinical evaluation, imaging tests, and laboratory analysis of the lymph fluid.
Treatment for Primary Intestinal Lymphangiectasia focuses on managing symptoms and preventing complications. This may involve dietary modifications, such as a low-fat, high-protein diet, along with the supplementation of essential nutrients. In severe cases, medications to reduce inflammation and swelling may be prescribed. Regular monitoring and follow-up with healthcare professionals are crucial to ensure optimal management of the condition.
If you suspect you or someone you know may have Primary Intestinal Lymphangiectasia, it is important to consult a healthcare professional for an accurate diagnosis and appropriate treatment plan.