Pulmonary atresia is a congenital heart defect characterized by the absence or severe narrowing of the pulmonary valve, which is responsible for regulating blood flow from the right ventricle to the lungs. This condition obstructs the normal blood flow to the lungs, leading to various complications and symptoms.
Synonyms for pulmonary atresia:
Pulmonary atresia is often associated with other heart defects, such as a ventricular septal defect (VSD) or an atrial septal defect (ASD). These additional defects can affect the severity of symptoms and the overall prognosis.
Common symptoms of pulmonary atresia include cyanosis (bluish discoloration of the skin and lips), rapid breathing, fatigue, and poor weight gain. Infants with this condition may experience difficulty in feeding and exhibit signs of respiratory distress.
Diagnosis of pulmonary atresia typically involves a thorough physical examination, echocardiography, and other imaging tests to assess the heart's structure and blood flow. Treatment options depend on the severity of the condition and may include medications to improve blood flow, cardiac catheterization procedures, or open-heart surgery to repair or reconstruct the pulmonary valve.
Long-term management of pulmonary atresia involves regular follow-up visits with a cardiologist to monitor the heart's function and address any potential complications. In some cases, additional interventions or surgeries may be required as the child grows.
It is important to consult with a healthcare professional for an accurate diagnosis and appropriate treatment plan for pulmonary atresia.