Trimethylaminuria, also known as fish odor syndrome, is a metabolic disorder characterized by a strong body odor resembling rotten fish. The ICD-10 code for Trimethylaminuria is E88.8, which falls under the category of "Other specified metabolic disorders." In the previous ICD-9 coding system, Trimethylaminuria was classified under code 277.8, which represented "Other specified disorders of metabolism." Proper diagnosis and management are crucial for individuals with this condition.
Trimethylaminuria, also known as fish odor syndrome, is a rare metabolic disorder characterized by the inability to break down trimethylamine, a compound found in certain foods. This condition leads to a strong and unpleasant body odor resembling that of rotten fish. In the International Classification of Diseases, Tenth Revision (ICD-10), Trimethylaminuria is classified under code E88.8, which is the code for other specified metabolic disorders. This code is used for conditions that do not have a specific code assigned to them but still fall under the broader category of metabolic disorders.
In the International Classification of Diseases, Ninth Revision (ICD-9), Trimethylaminuria is classified under code 270.3. This code is used for trimethylaminuria specifically and falls under the broader category of disorders of amino-acid metabolism.
It is important to note that ICD-10 codes are currently the standard for medical coding and documentation, while ICD-9 codes have been largely phased out. Therefore, healthcare professionals primarily use the ICD-10 code E88.8 to identify and document cases of Trimethylaminuria.