Dermatofibrosarcoma Protuberans (DFSP) Synonyms:
Dermatofibrosarcoma Protuberans (DFSP) is a rare type of skin cancer that typically develops in the deep layers of the skin. It is characterized by slow-growing, firm, and raised tumors that often appear on the trunk, limbs, or head and neck regions. DFSP is also known by several synonyms, including:
- Bednar Tumor: This term is used to describe DFSP tumors that have areas of pigmentation.
- DFSP Fibrosarcomatous: This term is used when the tumor shows more aggressive features, such as increased cellularity and higher mitotic activity.
- DFSP Giant Cell Fibroblastoma: This term is used when the tumor contains giant cells, which are large, multinucleated cells.
- DFSP Pigmented: This term is used when the tumor has a darker color due to increased pigmentation.
- DFSP with Myoid Differentiation: This term is used when the tumor shows features of smooth muscle differentiation.
- DFSP with Neural Differentiation: This term is used when the tumor shows features of nerve tissue differentiation.
- DFSP with Osteoclast-like Giant Cells: This term is used when the tumor contains osteoclast-like giant cells, which are cells that resemble those found in bone tissue.
It is important to note that while these synonyms describe different variations of DFSP, they all refer to the same type of skin cancer. DFSP is typically treated with surgical removal of the tumor, and in some cases, additional treatments such as radiation therapy or targeted therapy may be recommended.