Retroperitoneal Fibrosis, also known as Ormond's Disease, is a rare condition characterized by the abnormal growth of fibrous tissue in the retroperitoneal space, which is the area behind the abdominal cavity. This fibrous tissue can gradually surround and compress nearby structures, such as the ureters, major blood vessels, and nerves.
Synonyms for Retroperitoneal Fibrosis:
Retroperitoneal Fibrosis is often referred to as Ormond's Disease or Ormond's Syndrome, named after the physician who first described it in 1948. The term "idiopathic" indicates that the cause of the fibrosis is unknown in most cases. However, it can also be associated with certain medications, infections, autoimmune disorders, or malignancies.
The symptoms of Retroperitoneal Fibrosis can vary depending on the extent of fibrous tissue growth and the structures affected. Common symptoms include:
Diagnosis of Retroperitoneal Fibrosis involves a combination of medical history evaluation, physical examination, imaging tests (such as CT scan or MRI), and sometimes a biopsy of the affected tissue. Treatment typically involves a multidisciplinary approach, including medications to reduce inflammation and fibrosis, surgical intervention to relieve any obstructions or repair damaged structures, and close monitoring of renal function.
In conclusion, Retroperitoneal Fibrosis, also known as Ormond's Disease, is a rare condition characterized by the abnormal growth of fibrous tissue in the retroperitoneal space. It can cause various symptoms and requires a comprehensive approach for diagnosis and treatment.