Dandy-Walker Syndrome, also known as Dandy-Walker Malformation or Dandy-Walker Complex, is a rare congenital brain disorder that affects the development of the cerebellum, which is the part of the brain responsible for coordinating movement and balance. This condition is characterized by the presence of a cystic enlargement of the fourth ventricle, a partial or complete absence of the cerebellar vermis (a structure that connects the two hemispheres of the cerebellum), and an abnormal accumulation of fluid in the brain.
Although Dandy-Walker Syndrome is the most commonly used term, it is important to note that there are several synonyms that refer to the same condition:
It is important to understand that Dandy-Walker Syndrome is a complex disorder with varying degrees of severity and associated symptoms. The condition can lead to developmental delays, motor coordination difficulties, intellectual disabilities, hydrocephalus (excessive accumulation of fluid in the brain), and other neurological complications.
Early diagnosis and appropriate medical management are crucial in optimizing the outcomes for individuals with Dandy-Walker Syndrome. Treatment may involve surgical interventions to address hydrocephalus, physical and occupational therapy to improve motor skills, and supportive care to address associated medical and developmental challenges.