Degos Disease, also known as Malignant Atrophic Papulosis, is a rare and serious condition that affects the blood vessels in the body. It primarily affects the small and medium-sized arteries, leading to the formation of characteristic skin lesions and potentially affecting various organs.
The exact cause of Degos Disease is unknown, and it predominantly affects adults between the ages of 20 and 50. The initial symptoms often involve the skin, with the appearance of small, red papules that evolve into characteristic porcelain-white, atrophic lesions with a central depression. These skin lesions typically spare the face and scalp.
While the skin manifestations are the most visible signs of Degos Disease, the condition can also affect internal organs such as the gastrointestinal tract, central nervous system, and heart. This can lead to severe complications, including abdominal pain, neurological deficits, and cardiac abnormalities.
Diagnosis of Degos Disease can be challenging due to its rarity and similarity to other conditions. A skin biopsy and examination of affected tissues are often necessary for confirmation. Unfortunately, there is currently no known cure for Degos Disease, and treatment mainly focuses on managing symptoms and preventing complications.
It is crucial for individuals with Degos Disease to receive ongoing medical care and monitoring to address potential complications and improve quality of life.