What is the prevalence of Dermatofibrosarcoma Protuberans (DFSP)?
How many people does Dermatofibrosarcoma Protuberans (DFSP) affect? Does it have the same prevalence in men and women? And in the different countries?
Dermatofibrosarcoma Protuberans (DFSP) is a rare type of skin cancer that arises from the dermis layer of the skin. It accounts for approximately 1% of all soft tissue sarcomas. DFSP affects both males and females equally and typically occurs in young to middle-aged adults. The prevalence of DFSP is estimated to be around 4.2 cases per million people per year. Although it is a relatively uncommon cancer, early diagnosis and treatment are crucial for better outcomes.
Dermatofibrosarcoma Protuberans (DFSP) is a rare type of skin cancer that arises from the dermis, the second layer of the skin. It is characterized by slow-growing, firm, and raised tumors that typically appear on the trunk, limbs, or head and neck regions. DFSP is more commonly diagnosed in adults, with a peak incidence occurring between the ages of 20 and 50.
The prevalence of DFSP is relatively low compared to other types of skin cancers. It accounts for approximately 1% of all soft tissue sarcomas. The exact number of cases worldwide is difficult to determine due to its rarity and variations in reporting. However, it is estimated that DFSP affects around 0.8 to 5 individuals per million population annually.
Although DFSP is considered a low-grade malignancy, it has a high recurrence rate if not completely excised during surgery. Early diagnosis and appropriate treatment are crucial for optimal outcomes. Treatment options may include surgical removal, radiation therapy, and targeted therapies such as imatinib for advanced or unresectable cases.
Posted Sep 12, 2017 by Deana 2000
