Primary Intestinal Lymphangiectasia, also known as Waldmann's disease or Waldmann's syndrome, is a rare disorder characterized by abnormal dilation of the lymphatic vessels in the small intestine. This condition leads to the leakage of lymph fluid into the intestinal lumen, resulting in protein-losing enteropathy.
Protein-losing enteropathy is a significant feature of Primary Intestinal Lymphangiectasia, where the lymphatic vessels fail to properly absorb proteins from the intestine, leading to their loss in the stool. This can result in malnutrition, edema, and other complications.
Primary Intestinal Lymphangiectasia is also referred to as Waldmann's disease or Waldmann's syndrome, named after the German physician Georg Waldmann who first described the condition in 1961. The term "lymphangiectasia" refers to the abnormal dilation of lymphatic vessels, which is the hallmark of this disorder.
Other less commonly used synonyms for Primary Intestinal Lymphangiectasia include:
These synonyms are used interchangeably to describe the same condition characterized by abnormal dilation of the lymphatic vessels in the small intestine.