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What is the prevalence of Adenoid Cystic Carcinoma?
How many people does Adenoid Cystic Carcinoma affect? Does it have the same prevalence in men and women? And in the different countries?
Adenoid Cystic Carcinoma (ACC) is a rare form of cancer that primarily affects the salivary glands, but can also occur in other areas like the breast, trachea, or lacrimal glands. ACC accounts for approximately 1% of all head and neck malignancies. Although it is considered a rare cancer, it has a slow-growing nature and tends to recur over time. The prevalence of ACC varies depending on the location, with salivary gland ACC being the most common. Early detection and proper treatment are crucial for managing this challenging disease.
Adenoid Cystic Carcinoma (ACC) is a rare type of cancer that typically arises in the salivary glands, although it can also occur in other areas such as the breast, lacrimal glands, or trachea. ACC accounts for approximately 1% of all head and neck malignancies. While it is considered a rare cancer, its prevalence varies depending on the location of the tumor. In the salivary glands, ACC represents about 10-15% of all salivary gland tumors.
Although rare, ACC has a distinctive clinical behavior. It tends to grow slowly but persistently, often invading surrounding tissues and nerves. This aggressive nature contributes to its high recurrence rate and the potential for distant metastasis, particularly to the lungs and bones. ACC commonly affects individuals between the ages of 30 and 60, with a slight female predominance.
Due to its rarity and diverse presentation, diagnosing ACC can be challenging. Treatment typically involves a multidisciplinary approach, including surgery, radiation therapy, and sometimes chemotherapy. Despite advancements in treatment options, the long-term prognosis for ACC remains guarded, with a 10-year survival rate of approximately 50%.
In conclusion, while Adenoid Cystic Carcinoma is a rare cancer, its prevalence varies depending on the location of the tumor. Its distinctive clinical behavior and potential for aggressive growth make it a challenging disease to manage effectively.
Diseasemaps
Adenoid Cystic Carcinoma represents approximately .0025% of cancers diagnosed in the United States yearly, or 1200 people. Of all ages.
Posted May 19, 2017 by Carmenita 2650
ACC is a relatively rare malignant salivary gland tumor comprising less than 1% of all malignancies of head and neck.
Posted May 21, 2017 by Jen 2310
Adenoid cystic carcinoma (ACC) is an uncommon form of malignant neoplasm that arises within secretory glands, most commonly the major and minor salivary glands of the head and neck. Other sites of origin include the trachea, lacrimal gland, breast, skin, and vulva.
Posted Oct 17, 2017 by Peter 2500
