What is the prevalence of Dandy-Walker Syndrome?
How many people does Dandy-Walker Syndrome affect? Does it have the same prevalence in men and women? And in the different countries?
Dandy-Walker Syndrome is a rare congenital brain malformation characterized by the enlargement of the fourth ventricle, absence or underdevelopment of the cerebellar vermis, and cyst formation near the base of the skull. It affects approximately 1 in every 25,000 to 35,000 live births, making it a relatively uncommon condition. The prevalence may vary across different populations and regions. Dandy-Walker Syndrome can lead to various neurological and developmental issues, requiring specialized medical care and support for affected individuals.
Dandy-Walker Syndrome is a rare congenital brain malformation that affects the development of the cerebellum, which is responsible for coordinating movement and balance. It is characterized by the enlargement of the fourth ventricle, a fluid-filled cavity in the brain, and the absence or underdevelopment of the cerebellar vermis, the part of the cerebellum that connects its two hemispheres.
The prevalence of Dandy-Walker Syndrome is estimated to be around 1 in 25,000 to 35,000 live births. However, it is important to note that the exact prevalence may vary across different populations and regions. The condition is more commonly diagnosed in females than males, with a ratio of approximately 3:1.
Although Dandy-Walker Syndrome is considered a rare disorder, it can have significant neurological and developmental consequences. Individuals with this syndrome may experience a wide range of symptoms, including motor delays, intellectual disabilities, hydrocephalus (excessive accumulation of fluid in the brain), and problems with coordination and balance.
Early diagnosis and appropriate medical interventions, such as surgical treatments for hydrocephalus, can help manage the symptoms and improve the quality of life for individuals with Dandy-Walker Syndrome.
